自身炎症性疾病2013-6-22原发性免疫缺陷病PID由于先天因素(多为遗传因素)引起免疫器官、免疫活性细胞和免疫活性分子等构成成分发生缺陷，致使免疫反应缺如或降低，导致机体抗感染免疫功能低下的一组临床综合征联合免疫缺陷病 (combined T-cell and B-cell immunodeficiencies)以抗体为主的缺陷病 (predominantly antibody deficiencies)其他明确定义的免疫缺陷综合征 (other well defined immunodeficiency syndromes)免疫调节失衡性疾病 (diseases of immune dysregulation)吞噬细胞数量和/或功能缺陷病 (congenital defects of phagocyte number, function, or both)固有免疫缺陷病 (defects in innate immunity)自身炎症性疾病 (autoinflammatory disorders, AIDs)补体缺陷病 (complement deficiencies) PID
