临床分型临床分型l多发性肌炎多发性肌炎l皮肌炎皮肌炎l免疫介导坏死性免疫介导坏死性肌炎肌炎l肿瘤相关性肌炎肿瘤相关性肌炎lCTD相关性肌炎相关性肌炎l嗜酸性粒细胞肌炎嗜酸性粒细胞肌炎l肉芽肿性肌炎肉芽肿性肌炎l局灶局灶/结节性结节性肌炎肌炎l眶周眶周肌炎肌炎l包涵包涵体肌炎体肌炎多发性肌炎多发性肌炎(PM)(PM)l典型皮疹有诊断特异性典型皮疹有诊断特异性l合并合并ILDILD常见且进展快常见且进展快l难治性皮疹考虑合并肿难治性皮疹考虑合并肿瘤可能瘤可能皮肌炎皮肌炎(DM)无肌病性皮肌炎无肌病性皮肌炎(ADM)(ADM)l是一组高度异质性疾病是一组高度异质性疾病lNearly all patients will present with subacute onset of proximal weakness that is very symmetrical and involves the pelvic as well as the shoulder girdlel病病理理：肌肌肉肉的的坏坏死死是是其其突突出出临临床床表现表现,炎性浸润可以很轻或不炎性浸润可以很轻或不明显明显l预后因病
